Undifferentiated pleomorphic sarcoma associated with desmoid fibromatosis of soft tissues

Atypical clinical presentations of desmoid fibromas are exceedingly rare, and descriptions of the tumor’s progression in such cases are of particular interest. There are isolated publications documenting the potential development of post-radiation soft tissue sarcomas following radiological treatment for desmoid fibroma. However, the presented clinical case of sarcoma development in a 22-year-old patient with an extra-abdominal desmoid fibroma distinguishes itself from these reports due to the absence of a history of remote radiation therapy in her anamnesis.