Annaliis Lehto, Andreas Zapf, Andreas Hermann, J. Machts, Stefan Vielhaber, Jonas Koppenbrink, D. Edbauer, Elisabeth Kasper, Johannes Prudlo
2026.1.2Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration
tlooto Summary
It is found that the proportion of cognitively or behaviorally impaired patients was higher in the high-risk group of homozygous C-allele carriers and informant ratings suggested higher disinhibition in the C/C carriers, indicating that the C/C risk variant of UNC13A rs12608932 may contribute to general cognitive vulnerability rather than domain-specific deficit.
Abstract
The common single nucleotide polymorphism (SNP) rs12608932 located at a cryptic splice in the UNC13A gene has been reported to modify the clinical phenotype of ALS, but it is unclear whether homozygosity for the C-allele at UNC13A rs12608932 modifies specific domains of cognition in ALS. We analyzed retrospective data from a German cohort and found that the proportion of cognitively or behaviorally impaired patients was higher in the high-risk group of homozygous C-allele carriers. Patients with C/C alleles had lower scores than controls on verbal fluency, executive functioning, and delayed memory recall, but did not differ significantly from other ALS genotypes. Furthermore, informant ratings suggested higher disinhibition in the C/C carriers. These findings indicate that the C/C risk variant of UNC13A rs12608932 may contribute to general cognitive vulnerability rather than domain-specific deficit.
Citation format
LEHTO, Annaliis, et al. Homozygosity for the c allele at UNC13A rs12608932 seems to compromise cognition in ALS independently of the cognitive domains. Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration, 2026, 27(3-4): 348–351.