Diagnosis and management of congenital portosystemic shunts in children

As a rare portal vein vascular malformation, congenital portosystemic shunt leads to severe complications, including infantile cholestasis, hepatic tumor, portosystemic encephalopathy, hepatopulmonary syndrome and portopulmonary hypertension. Early recognition and prompt therapy prevent and reverse clinically significant complications and improve the long-term outcomes in children. Key words: Child; Congenital portosystemic shunts; Portal vein